Dentistry

Clinical manifestations and dental management of dentinogenesis imperfecta associated with osteogenesis imperfecta

19^th American Dental Congress

December 08-10, 2016 Phoenix, USA

Halima Abukabbos

University of Florida College of Dentistry, USA

Posters & Accepted Abstracts: Dentistry

Abstract:

Dentinogenesis imperfecta (DI) associated with osteogenesis imperfecta (OI) is a genetic disorder that affects the connective tissues and results in dentine dysplasia. DI results in structural defects in dentin formation in the deciduous or both deciduous and permanent dentitions. The incidence of DI is 1 in 8000. OI, also known as �??�??brittle bone disease�?� is a genetic disorder that affects the connective tissues. A person with OI experiences recurrent, multiple bone fractures. Different types of OI have been recognized, but most are due to mutations in the COL1A1 and COL1A2 genes, which encode the pro-alpha 1 and 2 polypeptide chains of type I collagen. Ligaments, sclera, bone, and dentin are mainly affected. This case report discusses the systemic and dental manifestations of OI and DI in a 4-year-old child, with moderate presentation of the disorder. Dental treatment included the use of strip and stainless-steel crowns under local anesthesia, as well as behavior modification techniques. Rigorous home care instructions, including reinforcement of the oral hygiene practice and avoidance of any episode that may lead to bone fracture, were discussed with the parents. The case was reevaluated at 3-month follow-up visits, wherein the medical and dental histories were updated, the child�??s growth was monitored, periodic clinical and radiographic examinations were performed, and the oral hygiene was evaluated via the debris index score and caries risk assessment. Further treatment of the permanent dentition may be needed in the future.

Biography :

Email: h_kabbos@hotmail.com