Dental Management of Dysostosis Cleidocranialis-Case Report

Ambarkova Vesna, Margarita Meskova, Igor Stankov, Karakamcev Vasko, Karakamcev Tomo, Popovski Vladimir

Cleidocranial dysplasia (CCD) is an autosomal dominant disorder characterized by skeletal anomalies such deformities, short stature of milder degree, abnormal shoulder mobility due to hypoplastic or aplastic clavicles. Cleidocranial dysplasia is characterized by anomalies of the thorax, spine, pelvis and extremities. Of particular interest to us as dentists are disturbances of the skull and tooth development. Case presentation: A 15 year-old girl with cleidocranial dysplasia (CCD) presented in this article, had typical features of CCD: delayed tooth eruption, underdeveloped upper jaw, especially premaxilla, high arched palate and a large number of excessive teeth. According to the patient’s age and clinical findings, fixed bridges prosthesis made of Ceramill CAD/CAM Sintron in both arches was the treatment of choice. Successful treatment of the orofacial problems of patient with CCD requires the combined efforts of several dental specialists. The case reported proves the efficacy of surgical, orthodontic and prosthodontic procedures in resolving of clinical dentofacial features of CCD.