Purpose: To describe a case of hypertensive chorioretinopathy due to secondary hypertension caused by primary renal artery stenosis. Method: Case report by reviewing medical data. Case report: Thirteen years old male, in treating for severe hypertension, presenting substantial bilateral visual impairment one month ago. During ophthalmologic examination, best corrected visual acuity in both eyes was 20/100 and hypertensive chorioretinopathy was found at the fundoscopic examination. Fundus photography, fluorescein angiography and optical coherence tomography were performed. Imaging tests showed left renal artery stenosis and a smaller left kidney. After clinical pharmacological treatment for artherial hypertension there was a slight improvement in visual acuity. Conclusion: Primary renal artery stenosis unilateral is a condition uncommon which can evolve with hypertensive chorioretinopathy.